Heme Synthesis
Succinyl Coenzyme A + Glycine
Delta-aminolevulinic
acid synthetase
Vitamin B
6
Delta-aminolevulinic acid
Porphobilinogen
Uroporphyrinogen III
Coproporphyrinogen III
Protoproporphyrinogen IX
Protoporphyrin IX
Fe
++
Heme
Mitochondria
cytoplasm
Mitochondria