Abnormal Hemoglobins
Hemoglobin Bart’s
Hemoglobin H
Hemoglobin S
4 gamma chains (4g) or g4
4 beta chains (4b) or b4
Trait
a2b1b6 glutamic acid           valine
Disease
a2b6 glutamic acid               valine
Hemoglobin C
Trait
a2b1b6 glutamic acid           lysine
Disease
a2b6 glutamic acid               lysine
Hemoglobin SC
Disease
A2b6 glutamic acid           valine  b6 glutamic acid             lysine