Abnormal Hemoglobins
Hemoglobin Bart’s
Hemoglobin H
Hemoglobin S
4 gamma chains (4
g
) or
g
4
4 beta chains (4
b
) or
b
4
Trait
a
2
b
1
b
6
glutamic acid
valine
Disease
a
2
b
6
glutamic acid
valine
Hemoglobin C
Trait
a
2
b
1
b
6
glutamic acid
lysine
Disease
a
2
b
6
glutamic acid
lysine
Hemoglobin SC
Disease
A
2
b
6
glutamic acid
valine
b
6
glutamic acid
lysine