What does it do?
Increased deposits of mucopolysaccharides (lipids)
in cytoplasm
Abnormality:
Decreased breakdown of mucopolysaccharides.
Deep purple to lilac colored granules called “Alder-
Reilly bodies”
Appearance:
Disorders:
Hunter’s syndrome: also called MPS II
Alder-Reilly Anomaly
Hurler’s syndrome: also called MPS I