Agnogenic Myeloid Metaplasia-3
Androgen therapy for severe anemia
Therapy:
Glucosteroids for hemolytic anemia
Hydroxyurea, interferon-a and –g, radiation
Splenectomy to relieve pain, portal hypertension, and thrombocytopenia
Busulfate for reduction of fibrosis & hypercellularity
For severe splenic pain:
Prognosis:
Depends on severity of anemia & thrombocytopenia:
Median = 5 years
15 years possible