Alpha Granule Deficiencies - 1
Alternate name:
Proteins formed in megakaryocyte such as:
Gray platelet syndrome
Platelet-derived growth hormone
Components stored in alpha granules:
Thrombospondin
Platelet factor 4
Albumin
IgG
Proteins in plasma and stored in granule such as:
Fibrinogen
Clinical symptoms:
Lifelong mild bleeding episodes
Moderate thrombocytopenia
Large gray-appearing platelets on blood smear